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lipidosis

DEFINITIONS OF: lipidosis

1

n a disorder of lipid metabolism; abnormal levels of certain fats accumulate in the body

Types:
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abetalipoproteinemia
a rare inherited disorder of fat metabolism; characterized by severe deficiency of beta-lipoproteins and abnormal red blood cells (acanthocytes) and abnormally low cholesterol levels
Gaucher's disease
a rare chronic disorder of lipid metabolism of genetic origin
Niemann-Pick disease
a disorder of lipid metabolism that is inherited as an autosomal recessive trait
Sachs disease, Tay-Sachs, Tay-Sachs disease, infantile amaurotic idiocy
a hereditary disorder of lipid metabolism occurring most frequently in individuals of Jewish descent in eastern Europe; accumulation of lipids in nervous tissue results in death in early childhood
Type of:
metabolic disorder
a disorder or defect of metabolism
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